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(9 Results)![Fabry & Myelinosomes, Art of Medicine](https://www.arkanalabs.com/wp-content/uploads/Fabry-digital-art-copy-432x288.jpg)
Art of Medicine: Fabry
The image above shows myelinosomes, also known as zebra bodies for their appearance on tangential sectioning. Myelinosomes are seen in…
![A-galactosidase A , pushing glass, arkana laboratories, kidney disease](https://www.arkanalabs.com/wp-content/uploads/1.-Low-mag-view-of-tissue-copy-432x288.jpg)
Pushing Glass (March 23, 2018)
These images are from the kidney biopsy of a 70-year-old woman with a history of hypertension and valvular heart disease…
![vacuolated cytoplasm, Fabry Disease in Female Carriers](https://www.arkanalabs.com/wp-content/uploads/Fig-1-copy-32-432x288.jpg)
Fabry Disease in Female Carriers
A renal biopsy was performed on a 51-year-old female with strong family history of Fabry disease and a known carrier…
![Fabry Disease](https://www.arkanalabs.com/wp-content/uploads/tp11.15-432x288.jpg)
Twitter Poll (November 15, 2017)
ANSWER: B Fabry disease causes a genetically derived deficiency in alpha-galactosidase A enzyme and accumulation of globotriaosylceramide (GL3).
![Fabry disease](https://www.arkanalabs.com/wp-content/uploads/Fig-1-copy-18-432x288.jpg)
Fabry Disease and IgA
A 34-year-old Asian female underwent a renal biopsy as part of the workup for progressively worsening renal function (Cr =…
![Fabry Disease](https://www.arkanalabs.com/wp-content/uploads/Fig-1-copy-7-432x288.jpg)
Fabrys
This biopsy shows glomeruli with visceral epithelial cells (podocytes) displaying ample vacuolated cytoplasm (Fig 1), which is highlighted on a…
![Fabry EM](https://www.arkanalabs.com/wp-content/uploads/FabryEMImage9-1-432x288.jpg)
Fabry EM
Electron photomicrograph of a glomerular podocyte showing the characteristic electron dense laminated inclusions of Fabry disease. Fabry is a lysosomal…